Yamamoto M, Hagihara H, Mogaki M, Iimuro Y, Fujii H, Ainota T, Akahane Y, Matsumoto Y
First Department of Surgery, Yamanashi Medical College, Japan.
J Gastroenterol. 1994 Aug;29(4):518-24. doi: 10.1007/BF02361254.
We report a rare case of mesenchymal hamartoma in the cirrhotic liver of a 52-year-old Japanese male. The tumor, 3.5 cm in diameter, contained a cystic lesion and was located in the lateral segment. Bile duct cystadenoma was considered most likely preoperatively because of the patient's age and the normal levels of tumor markers. However, since malignancy of the lesion could not be ruled out by preoperative imaging diagnosis, lateral segmentectomy was performed. Histological examination led to a diagnosis of mesenchymal hamartoma, since the lesion consisted of a multilocular abnormal bile duct accompanied by abundant myxomatous or loose collagen.
我们报告了一例罕见的间叶性错构瘤，发生于一名52岁日本男性的肝硬化肝脏。肿瘤直径3.5厘米，含有一个囊性病变，位于外侧段。由于患者年龄及肿瘤标志物水平正常，术前最可能考虑的是胆管囊腺瘤。然而，由于术前影像学诊断不能排除病变的恶性可能性，故实施了外侧段切除术。组织学检查诊断为间叶性错构瘤，因为病变由一个多房性异常胆管组成，并伴有大量黏液瘤样或疏松的胶原组织。
