[Unilateral congenital glaucoma and glioma of the optic nerve in the framework of neurofibromatosis 1].

A three and a half year-old boy with neurofibromatosis-1 was shown to have an unilateral glaucoma without other associated characteristics (homolateral facial hypertrophy, homolateral eyelid plexiform neuroma). This presentation is rare. Moreover, cerebral MRI disclosed a bilateral intraneural optic nerve glioma. The MRI of optic nerve glioma is discussed.