Igarashi Y, Watanabe Y, Aso S
Department of Otolaryngology, Toyama Medical and Pharmaceutical University, Japan.
ORL J Otorhinolaryngol Relat Spec. 1994 Sep-Oct;56(5):295-8. doi: 10.1159/000276678.
Behçet's disease is generally known as an autoimmune disease. We report a case of Behçet's disease who had fluctuating hearing loss, tinnitus and dizziness. A 37-year-old woman had bilateral hearing loss in low audiometric frequencies. Audiological and vestibular examinations revealed an inner ear lesion. The patient had an enlarged negative summation potential in the electrocochleogram and a positive glycerol test, which suggested endolymphatic hydrops. The pathological characteristic of Behçet's disease is thought to be vasculitis. So this case suggests an association of autoimmune vasculitis with endolymphatic hydrops.
白塞病通常被认为是一种自身免疫性疾病。我们报告一例患有波动性听力损失、耳鸣和头晕的白塞病病例。一名37岁女性在低听力频率出现双侧听力损失。听力学和前庭检查显示内耳病变。该患者在耳蜗电图中负和电位增大，甘油试验阳性，提示存在内淋巴积水。白塞病的病理特征被认为是血管炎。因此，该病例提示自身免疫性血管炎与内淋巴积水之间存在关联。
