Mainetti C, Masouyé I, Harms M, Saurat J H
Clinique de Dermatologie, Hôpital Cantonal Universitaire, Genève, Suisse.
Ann Dermatol Venereol. 1994;121(2):165-70.
We report a case of solid persistent facial oedema in a 18-year-old woman. A biopsy specimen from the nose demonstrating lympho-epithelioid granulomas and an electro-neuro-myographic examination revealing sub-clinical sequellae from an old right facial palsy, led to the definite diagnosis of Melkersson-Rosenthal syndrome (MRS). We focus on the differential diagnosis of persistent facial oedema and outline the difficulties to establish the diagnosis of MRS when all features of the classic triad "recurrent labial edema-facial nerve palsy-lingua plicata" are not present.
我们报告一例18岁女性持续性面部实性水肿病例。鼻部活检标本显示淋巴上皮样肉芽肿，神经电生理检查显示既往右侧面神经麻痹的亚临床后遗症，最终确诊为梅尔克森－罗森塔尔综合征（MRS）。我们着重探讨持续性面部水肿的鉴别诊断，并概述在经典三联征“复发性唇部水肿－面神经麻痹－皱襞舌”的所有特征均未出现时，确立MRS诊断的困难之处。
