Emmert-Buck M R, Stay E J, Tsokos M, Travis W D
Department of Surgical Pathology, National Cancer Institute, Bethesda, Md 20892.
Arch Pathol Lab Med. 1994 Dec;118(12):1220-2.
Pulmonary artery rhabdomyosarcomas are rare lesions, with a small number of cases reported in the literature. We report a case of pulmonary artery rhabdomyosarcoma that arose in the right pulmonary artery. The patient presented with cough, chest pain, and hemoptysis and was found to have a sarcoma arising in the right pulmonary artery and extending distally within the pulmonary vasculature into the right lung. The gross pathologic features, microscopic appearance, immunohistochemical profile, and computed tomographic and electron microscopic findings are presented. The site of origin and differential diagnosis of these lesions are discussed.
肺动脉横纹肌肉瘤是罕见的病变，文献中报道的病例较少。我们报告一例起源于右肺动脉的肺动脉横纹肌肉瘤。患者表现为咳嗽、胸痛和咯血，经检查发现右肺动脉有肉瘤，并在肺血管系统内向远端延伸至右肺。文中介绍了大体病理特征、显微镜下表现、免疫组化特征以及计算机断层扫描和电子显微镜检查结果。并对这些病变的起源部位和鉴别诊断进行了讨论。
