Cherian K M, Rao S G
Institute of Cardiovascular Diseases, Madras.
Indian Heart J. 1994 Mar-Apr;46(2):91-5.
Partially or totally unroofed coronary sinus is usually associated with other anomalies of the heart. In the period of 5 years between January 1987 to October 1992, 13 patients with this syndrome were encountered. All of them had a left superior vena cava draining into left atrium. Of these, 12 were totally unroofed and one had a partial unroofing of the coronary sinus. Associated anomalies encountered included common atria, cortriatriatum, complete A-V canal, tetralogy of Fallot, total and hemianomalous pulmonary venous connection, double outlet right ventricle and atrial isomerism with dextrocardia. Four patients died in the post operative period due to low cardiac output. The nine survivors are all in NYHA class I. At a mean follow up of 4 years, all except one were in sinus rhythm. The other had a nodal rhythm persisting for 4 years. Pericardial baffle redirection of LSVC into the systemic venous atrium which is advocated, was performed in all but one of our earliest patients. Unroofed coronary sinus syndrome is a correctable lesion, the results of which are influenced more by the complexity of the associated anomalies rather than the syndrome per se.
部分或完全无顶冠状静脉窦通常与其他心脏异常相关。在1987年1月至1992年10月的5年期间，遇到了13例患有该综合征的患者。他们均有左上腔静脉引流至左心房。其中，12例为完全无顶，1例为冠状静脉窦部分无顶。发现的相关异常包括共同心房、三房心、完全性房室通道、法洛四联症、完全性和部分性肺静脉异位连接、右心室双出口以及右旋心的心房异构。4例患者术后因低心输出量死亡。9名幸存者均为纽约心脏协会（NYHA）心功能I级。平均随访4年，除1例患者外，其余均为窦性心律。另1例患者的结性心律持续了4年。除了我们最早的1例患者外，其余所有患者均进行了将左上腔静脉经心包挡板重定向至体静脉心房的手术。无顶冠状静脉窦综合征是一种可矫正的病变，其结果更多地受相关异常的复杂性影响，而非该综合征本身。
