Bourgain C, Pierré E, De Vits A, Amy J J, Klöppel G
Department of Pathology, Academic Hospital Jette, Free University of Brussels, Belgium.
Pathol Res Pract. 1994 May;190(5):500-4; discussion 504-6.
Disseminated peritoneal leiomyomatosis (DPL) is a very rare disorder, characterized by the presence of multiple intraabdominal smooth muscle nodules and frequently associated with a high estrogen production. We report on a 43-year-old woman with DPL and simultaneous bilateral ovarian cystic teratomas. There were no overt endocrine abnormalities. Due to distinct cellular pleomorphism on a frozen section, complete removal of smooth muscle nodules was suggested, but could not be achieved because of severe bleeding. Two years after resection of the ovarian tumors but with residual DPL, the patient is doing well, with no evidence of malignant disease.
播散性腹膜平滑肌瘤病(DPL)是一种非常罕见的疾病,其特征是腹腔内存在多个平滑肌结节,且常与高雌激素分泌有关。我们报告了一名43岁患有DPL并同时患有双侧卵巢囊性畸胎瘤的女性。患者无明显内分泌异常。由于冰冻切片上细胞具有明显的多形性,建议完整切除平滑肌结节,但因严重出血未能实现。卵巢肿瘤切除两年后,患者仍有残留的DPL,但情况良好,无恶性疾病迹象。