García Aroca J, Sanz N, Alonso J L, de Mingo L, Rollán V
Servicio de Cirugía Pediátrica, Hospital Niño Jesús, Madrid.
Cir Pediatr. 1994 Jul;7(3):115-20.
The term intestinal pseudo-obstruction, is applied to a group of clinical disorders in which there are obstructive symptoms, in the absence of a mechanical agent, secondary to a disorder of intestinal motility. In this report, we show manometric studies done in four patients, with acute intestinal pseudo-obstructions, secondary to von Recklinghausen's neurofibromatosis (VRNF), in two patients, and in one patient with Duchenne's muscular dystrophy (DMD) and in another with Werdnig-Hoffmann's disease (WHD). We studied 24 hours antroduodenal motility, specially during phase 3 of the migratory motor complex (CMM), which showed a neuropathic disorder in one case of von Recklinghausen's disease and a myopathic disorder in patients with Duchenne's muscular dystrophy and Werdnig-Hoffmann's disease. We analysed results and conclusions and specially the kinetic action of erythromycin.
术语“肠道假性梗阻”用于描述一组临床病症,这些病症存在梗阻症状,但不存在机械性梗阻因素,而是继发于肠道动力障碍。在本报告中,我们展示了对4例患者进行的测压研究结果,其中2例急性肠道假性梗阻继发于冯·雷克林豪森神经纤维瘤病(VRNF),1例继发于杜兴氏肌营养不良症(DMD),另1例继发于韦尔-霍夫曼病(WHD)。我们研究了24小时的十二指肠动力,特别是移行性运动复合波(CMM)的第3相,结果显示1例冯·雷克林豪森病患者存在神经病变,而杜兴氏肌营养不良症和韦尔-霍夫曼病患者存在肌病性病变。我们分析了结果和结论,特别是红霉素的动力学作用。