持续性肌肉纤维活动综合征。11年随访的病例报告。

Syndrome of continuous muscle fiber activity. Case report with 11-year follow-up.

作者信息

de Oliveira J T, Levy-Reis I

机构信息

Neurology Service, Hospital of Clinics, Federal University of Minas Gerais, Medical School, Belo Horizonte, Brasil.

出版信息

Arq Neuropsiquiatr. 1994 Mar;52(1):96-9. doi: 10.1590/s0004-282x1994000100019.

DOI:10.1590/s0004-282x1994000100019

PMID:8002819

Abstract

A 16-year-old male patient who presented with muscle stiffness and dysphonia is described. Electromyography revealed continuous motor activity that was unaffected by peripheral nerve block or general anaesthesia, but was abolished by curare. The patient had a marked improvement after using phenytoin. The follow-up 11-years later corroborates with the proposed benignity of this syndrome, in spite of being dependent on medication.

摘要

本文描述了一名16岁男性患者，其表现为肌肉僵硬和发音困难。肌电图显示持续的运动活动，不受周围神经阻滞或全身麻醉影响，但可被箭毒消除。该患者使用苯妥英钠后有明显改善。尽管依赖药物治疗，但11年后的随访证实了该综合征的良性特征。