Saca L F, Szer I S, Henar E, Nanjundiah P, Haddad Z H, Quismorio F P
Department of Pediatrics, Los Angeles County, School of Medicine, CA.
J Rheumatol. 1994 Mar;21(3):545-8.
Budd-Chiari syndrome, hypertension, and thrombocytopenia developed in a 6-year-old girl as manifestations of primary antiphospholipid antibody syndrome (APS). She improved with systemic corticosteroid and anticoagulation therapy. Anticardiolipin antibodies were found in the patient, her mother and 3 siblings, suggesting the importance of genetic factors. The clinical features of an APS in children is reviewed.
一名6岁女孩出现布加综合征、高血压和血小板减少症，这些是原发性抗磷脂抗体综合征（APS）的表现。她通过全身皮质类固醇和抗凝治疗后病情好转。在该患者、其母亲和3个兄弟姐妹体内均发现了抗心磷脂抗体，提示遗传因素的重要性。本文对儿童APS的临床特征进行了综述。
