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A case of Creutzfeldt-Jakob disease presenting with cortical deafness.

作者信息

Tobias E, Mann C, Bone I, de Silva R, Ironside J

出版信息

J Neurol Neurosurg Psychiatry. 1994 Jul;57(7):872-3. doi: 10.1136/jnnp.57.7.872.

DOI:10.1136/jnnp.57.7.872
PMID:8021690
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC1073046/
Abstract
摘要

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Three cases of Creutzfeldt-Jakob disease presenting with a predominant dysexecutive syndrome.三例以执行功能障碍为主的克雅氏病。
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Acute auditory agnosia as the presenting hearing disorder in MELAS.急性听觉失认作为线粒体脑肌病伴乳酸血症和卒中样发作(MELAS)的首发听力障碍
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Distinct neuropsychological characteristics in Creutzfeldt-Jakob disease.克雅氏病独特的神经心理学特征。
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本文引用的文献

1
Cortical deafness--a case report and review of the literature.
J Neurol Sci. 1980 Oct;48(1):35-49. doi: 10.1016/0022-510x(80)90148-3.
2
A retrospective study of Creutzfeldt-Jakob disease in England and Wales 1970-79. I: Clinical features.1970 - 1979年英格兰和威尔士克雅氏病的回顾性研究。I:临床特征。
J Neurol Neurosurg Psychiatry. 1984 Feb;47(2):134-40. doi: 10.1136/jnnp.47.2.134.
3
Visual evoked potentials in acute occipital blindness. Diagnostic and prognostic value.急性枕叶盲的视觉诱发电位。诊断及预后价值。
J Neurol. 1982;227(4):193-200. doi: 10.1007/BF00313386.
4
Parkinson's disease: a genetic study.帕金森病:一项遗传学研究。
Can J Neurol Sci. 1986 Aug;13(3):248-51. doi: 10.1017/s0317167100036362.
5
'So-called' cortical deafness. Clinical, neurophysiological and radiological observations.“所谓的”皮质性聋。临床、神经生理学及放射学观察
Brain. 1991 Dec;114 ( Pt 6):2385-401. doi: 10.1093/brain/114.6.2385.
6
The role of individual human cytochromes P450 in drug metabolism and clinical response.个体人类细胞色素P450在药物代谢和临床反应中的作用。
Trends Pharmacol Sci. 1992 Dec;13(12):434-9. doi: 10.1016/0165-6147(92)90140-2.