Sekul E A, Moak J P, Schultz R J, Glaze D G, Dunn J K, Percy A K
Department of Pediatrics, Baylor College of Medicine, Houston, Texas 77030.
J Pediatr. 1994 Jul;125(1):80-2. doi: 10.1016/s0022-3476(94)70128-8.
Girls with Rett syndrome had significantly longer corrected QT intervals (p < 0.001) and more T-wave abnormalities (p < 0.001) than were found in age-matched healthy girls. With advancing stages of the syndrome, the proportion of corrected QT interval prolongations and T-wave changes increased. The findings suggest a possible cardiac basis for sudden, unexpected death in Rett syndrome.
患有雷特综合征的女孩比年龄匹配的健康女孩有明显更长的校正QT间期（p < 0.001）和更多的T波异常（p < 0.001）。随着该综合征病情的进展，校正QT间期延长和T波改变的比例增加。这些发现提示雷特综合征中突然意外死亡可能存在心脏方面的原因。
