Eshel G, Vinograd I, Barr J, Zemer D
Paediatric Intensive Care Unit, Assaf Harofeh Medical Centre, Zerifin, Israel.
Br J Surg. 1994 Jun;81(6):894-6. doi: 10.1002/bjs.1800810633.
Twenty-nine children with familial Mediterranean fever presented with 39 attacks of acute scrotal pain. Of these, 25 patients had an acute scrotum complicating familial Mediterranean fever and only four had testicular torsion. Scrotal pain was the only manifestation of a familial Mediterranean fever crisis in 36 episodes and in 15 boys scrotal involvement was the first manifestation of the condition. Fourteen patients were treated medically. Of 15 patients who underwent scrotal exploration there were no definite diagnostic findings in 11 and four had testicular torsion. Three cardinal features strongly suggest the diagnosis of acute scrotum in familial Mediterranean fever in a boy of Mediterranean origin with a relevant family history: recurrent scrotal pain or swelling; body temperature above 37.5 degrees C; and gradual onset of pain, usually of more than 12 h duration. Conservative management can safely be undertaken in these boys without fear of losing a salvageable testis.
29名家族性地中海热患儿出现了39次急性阴囊疼痛发作。其中，25例患者的急性阴囊病变并发家族性地中海热，仅有4例发生睾丸扭转。在36次发作中，阴囊疼痛是家族性地中海热危机的唯一表现，15名男孩中阴囊受累是该病的首发表现。14例患者接受了药物治疗。在15例接受阴囊探查的患者中，11例未发现明确的诊断结果，4例发生睾丸扭转。对于有相关家族史的地中海裔男孩，三个主要特征强烈提示家族性地中海热伴急性阴囊病变的诊断：反复出现的阴囊疼痛或肿胀；体温高于37.5摄氏度；疼痛逐渐发作，通常持续超过12小时。对这些男孩进行保守治疗是安全的，不用担心失去可挽救的睾丸。
