Murphy G F, Miller S D, Kenady D E, O'Connor W, Wood D P, McRoberts J W, Gee W F
Division of Urology, University of Kentucky Medical Center, Lexington.
Urology. 1994 Aug;44(2):273-7. doi: 10.1016/s0090-4295(94)80150-9.
Extra-adrenal pheochromocytomas and paragangliomas are rare tumors of neural crest origin, most commonly found in the retroperitoneum. Because these tumors are so uncommon, relatively little is known about their natural history. Comparisons between adrenal pheochromocytomas and extra-adrenal pheochromocytomas have appeared in the medical literature. Like pheochromocytomas, paragangliomas may occur as functional or nonfunctional tumors. Furthermore, although the hereditary occurrence of pheochromocytomas is well documented, the familial nature of paragangliomas is unclear. We present the first report of a mother and son with nonfunctional paragangliomas occurring in the same anatomic location and describe their care and treatment.
肾上腺外嗜铬细胞瘤和副神经节瘤是起源于神经嵴的罕见肿瘤，最常见于腹膜后。由于这些肿瘤非常罕见，对其自然病史了解相对较少。医学文献中已出现肾上腺嗜铬细胞瘤与肾上腺外嗜铬细胞瘤的比较。与嗜铬细胞瘤一样，副神经节瘤可表现为功能性或无功能性肿瘤。此外，虽然嗜铬细胞瘤的遗传性已有充分记录，但副神经节瘤的家族性性质尚不清楚。我们首次报告了一对母子在相同解剖位置发生无功能性副神经节瘤的病例，并描述了他们的诊治情况。
