Jenkins P
Nurs Times. 1994;90(34):40-1.
This paper describes a method of liver transplantation in which only one segment from a donor organ is used to replace one part of the recipient's own liver. The patient was a nine-year-old boy with Crigler-Najjar, a rare inborn error of metabolism, in which the enzyme needed to conjugate bile is absent. The technique of orthotopic liver segment replacement is described, and the possibilities of using this procedure to help patients with some other inherited metabolic disorders is discussed. When this paper was written, the procedure has been performed only once before, on an adult in the USA.
本文描述了一种肝移植方法，即仅使用供体器官的一个肝段来替代受体自身肝脏的一部分。患者是一名9岁男孩，患有克里格勒-纳贾尔综合征，这是一种罕见的先天性代谢紊乱疾病，体内缺乏结合胆汁所需的酶。文中描述了原位肝段置换技术，并讨论了使用该方法帮助其他一些遗传性代谢紊乱患者的可能性。撰写本文时，该手术此前仅在美国对一名成年人实施过一次。
