Provenier F, Jordaens L
Universitair Ziekenhuis, Afd. Cardiologie, Gent, België.
Ned Tijdschr Geneeskd. 1993 Jan 16;137(3):138-41.
An anomalous left coronary artery originating from the pulmonary artery is a rare, but frequently lethal congenital disorder. A wide range of symptoms due to heart failure and myocardial ischaemia may appear soon after birth. We describe a young woman who was admitted to the hospital after resuscitation for ventricular fibrillation. An anomalous origin of the left coronary artery from the pulmonary trunk was diagnosed. An echocardiographic evaluation in this adult patient illustrated the haemodynamic disturbances in the coronary circulation. The thallium scintigram showed reversible perfusion defects on exercise. Ischaemia may be implicated in the pathogenesis of the arrhythmia. Our patient was treated with an arterial graft and ligation of the left coronary artery at its origin.
起源于肺动脉的异常左冠状动脉是一种罕见但常致命的先天性疾病。出生后不久可能就会出现因心力衰竭和心肌缺血导致的一系列症状。我们描述了一名年轻女性，她在因室颤复苏后入院。诊断为左冠状动脉起源于肺动脉干异常。对该成年患者的超声心动图评估显示了冠状动脉循环中的血流动力学紊乱。铊闪烁扫描显示运动时可逆性灌注缺损。缺血可能与心律失常的发病机制有关。我们的患者接受了动脉移植及在左冠状动脉起始处结扎的治疗。
