Davio P, Casagranda I, Moroni M, Porta C, Ratto C, Cosimi M F, Bobbio-Pallavicini E
Divisione di Medicina Generale, Ospedale Civile, Tortona.
Recenti Prog Med. 1993 Dec;84(12):850-4.
Behçet's disease is a chronic, heterogeneous, multisystem disorder caused by a vasculitis involving arterial and venous vessels of all sized. In 1990, a new set of diagnostic criteria has been proposed as a guide to diagnosis of Behçet's disease, requiring the presence of oral ulcerations plus two of the following symptoms or signs: genital ulcerations, characteristics eye lesions, typical skin lesions, and a positive pathergy test. Nevertheless, both clinic and pathologic diagnosis of Behçet's disease remains sometimes very difficult. Diagnostic procedures and therapeutic implications in a case of Behçet's disease are reported and discussed.
白塞病是一种由涉及各种大小动静脉的血管炎引起的慢性、异质性、多系统疾病。1990年,一套新的诊断标准被提出作为白塞病诊断的指南,要求存在口腔溃疡并伴有以下症状或体征中的两项:生殖器溃疡、特征性眼部病变、典型皮肤病变以及针刺试验阳性。然而,白塞病的临床和病理诊断有时仍然非常困难。本文报告并讨论了一例白塞病患者的诊断程序和治疗意义。