Mach J, Grézl M, Veselý J, Navrátil P
Interní oddĕlení nemocnice a polikliniky, Sumperk.
Vnitr Lek. 1994 Feb;40(2):108-10.
The authors describe a typical echocardiographic finding in restrictive infiltrative cardiomyopathy which after two years led to the diagnosis of primary amyloidosis in a 51-year-old woman. The predominating manifestations of the disease were renal damage with final failure, heart failure, monoclonal gammapathy and damage of other organs. Aimed treatment of amyloidosis and repeated haemodialysis did not prevent the patient's death from cardiac and renal failure. Primary amyloidosis was confirmed by histological examination and necropsy.
作者描述了一名51岁女性限制性浸润性心肌病的典型超声心动图表现，两年后该表现导致原发性淀粉样变性的诊断。该疾病的主要表现为肾脏损害并最终衰竭、心力衰竭、单克隆丙种球蛋白病以及其他器官损害。针对淀粉样变性的治疗及反复血液透析未能阻止患者死于心脏和肾衰竭。组织学检查和尸检证实为原发性淀粉样变性。
