Miyaji K, Shimada M, Sekiguchi A, Nishimura K, Ishizawa A, Isoda T, Senzaki H, Hishitani T
Department of Cardiovascular Surgery, National Children's Hospital, Tokyo, Japan.
Kyobu Geka. 1994 Apr;47(4):307-10.
Successful repair was performed for a 7-year-old male with a diagnosis of partial anomalous pulmonary venous connection (PAPVC) to superior vena cava (SVC) and superior sinus venosus atrial septal defect (ASD). The SVC was divided above the orifice of the anomalous pulmonary vein and the cephalad end of the SVC was anastomosed directly to the right atrial appendage. A patch was used to divert pulmonary venous flow from the orifice of the SVC through superior sinus venosus ASD into the left atrium. Postoperative course was uneventful with normal sinus rhythm. There was no evidence of vena caval or pulmonary venous obstruction. At 3-month after surgery, sinus node function was confirmed to be normal by electrophysiological study. This is useful alternative method for repair of PAPVC to high or middle SVC.
为一名7岁男性成功实施了修复手术，该患者诊断为部分性肺静脉异位连接（PAPVC）至 superior vena cava（SVC）以及上腔静脉窦型房间隔缺损（ASD）。在异常肺静脉开口上方切断SVC，并将SVC的头端直接吻合至右心耳。使用补片将肺静脉血流从SVC开口经上腔静脉窦型ASD引流至左心房。术后过程平稳，窦性心律正常。无腔静脉或肺静脉梗阻的证据。术后3个月，通过电生理研究证实窦房结功能正常。这是修复PAPVC至高位或中位SVC的一种有用的替代方法。
