Uzzo R G, Libby D M, Vaughan E D, Levey S H
Department of Urology, James Buchanan Brady Foundation, New York Hospital-Cornell University Medical Center, New York.
J Urol. 1994 Jun;151(6):1612-5. doi: 10.1016/s0022-5347(17)35317-x.
A patient with tuberous sclerosis and known bilateral angiomyolipomas presented with a complete pneumothorax prior to scheduled renal surgery. Evaluation revealed the presence of pulmonary lymphangioleiomyoma, an unusual entity known to coexist with tuberous sclerosis. Pulmonary decortication and conservative renal surgery resulted in a satisfactory long-term result.
一名患有结节性硬化症且已知双侧肾血管平滑肌脂肪瘤的患者，在预定的肾脏手术前出现了完全性气胸。评估发现存在肺淋巴管平滑肌瘤，这是一种已知与结节性硬化症共存的罕见病症。肺纤维板剥脱术和保守性肾脏手术取得了满意的长期效果。
