斯蒂尔病在长期缓解后复发并伴有严重肺炎。

Still's disease relapse with severe pneumonitis after prolonged remission.

作者信息

Yoshinaga H, Koike R, Maruyama T, Iizuka H, Matsuoka H, Kubota T, Miyasaka N

机构信息

Department of Internal Medicine, Tokyo Medical and Dental University.

出版信息

Intern Med. 1993 Dec;32(12):902-5. doi: 10.2169/internalmedicine.32.902.

DOI:10.2169/internalmedicine.32.902

PMID:8204963

Abstract

A 20-year-old woman who had suffered from Still's disease was admitted for fever and progressive pneumonitis after long-term remission. High spiking fever, leukocytosis, splenomegaly and an extremely high serum ferritin concentration strongly suggested a relapse of Still's disease. Intensive therapy with high-dose methylprednisolone, cyclophosphamide and gamma globulin was required for the severe pneumonitis, which was thought to be a rare manifestation in Still's disease.

摘要

一名曾患斯蒂尔病的20岁女性，在长期缓解后因发热和进行性肺炎入院。高热、白细胞增多、脾肿大以及极高的血清铁蛋白浓度强烈提示斯蒂尔病复发。对于严重肺炎，需要大剂量甲基泼尼松龙、环磷酰胺和γ球蛋白进行强化治疗，这种严重肺炎被认为是斯蒂尔病中一种罕见的表现。