Lieu A S, Huang C J, Huang T J, Chai C Y
Department of Surgery, Kaohsiung Medical College, Taiwan, Republic of China.
Gaoxiong Yi Xue Ke Xue Za Zhi. 1993 Dec;9(12):698-702.
A 48-year-old female patient with von Recklinghausen's disease was admitted to Kaohsiung Medical College Hospital due to massive hematochezia. The emergent mesentery arteriography revealed multiple hypervascular small intestinal lesions but no contrast extravasation. The endoscopic examination revealed a blood-filled small intestine with normal colonic mucosa. Laparotomy was carried out and multiple extraluminal masses on antimesenteric side of the small intestine were found. Segmental resection of the small intestine resulted in resolution of her symptom. The largest mass was diagnosed as leiomyosarcoma, and the others were diagnosed as leiomyoma. Histologically, differential diagnosis between leiomyosarcoma and leiomyoma is not clear cut, because it is based on a number of differentiating features. Surgical resection is the treatment of choice for intestinal leiomyosarcoma. The long-term follow-up of this patient is mandatory.
一名患有冯雷克林霍增氏病的48岁女性患者因大量便血入住高雄医学院附设医院。紧急肠系膜动脉造影显示多处小肠高血运病变，但无造影剂外渗。内镜检查显示小肠充满血液，结肠黏膜正常。遂行剖腹手术，发现小肠系膜对侧有多个肠外肿块。小肠节段性切除后症状缓解。最大的肿块诊断为平滑肌肉瘤，其他为平滑肌瘤。在组织学上，平滑肌肉瘤和平滑肌瘤的鉴别诊断并不明确，因为这基于许多鉴别特征。手术切除是肠道平滑肌肉瘤的首选治疗方法。该患者必须进行长期随访。
