Nagane M, Tsuchida T, Takemura N, Hayakawa I
Department of Neurosurgery, Bokuto Municipal Hospital, Tokyo, Japan.
Surg Neurol. 1993 Oct;40(4):314-9. doi: 10.1016/0090-3019(93)90143-o.
Retroflexion of the hypoplastic fused cerebrum is a rare condition in holoprosencephaly. We describe a new case of this entity in a 7-year-old boy with alobar holoprosencephaly whi developed retroflexion of the holosphere 7 years after a ventriculo-peritoneal shunt was placed. The radiological findings revealed retroflexion of the cerebrum anchored to the cranial vault between the precerebral space and the dorsal sac, which were open to each other. In patients with holoprosencephaly, the possibility of retroflexion of the holosphere should be considered after placement of a ventriculo-peritoneal shunt for associated hydrocephalus.
发育不全的融合大脑后屈是全前脑畸形中的一种罕见情况。我们描述了一名7岁患叶状全前脑畸形男孩的这一病症新病例，该男孩在进行脑室 - 腹腔分流术后7年出现了脑球后屈。影像学检查结果显示，大脑后屈固定于前脑间隙和背侧囊之间的颅顶，二者相互连通。对于全前脑畸形患者，在因相关脑积水进行脑室 - 腹腔分流术后，应考虑脑球后屈的可能性。
