Steffens K, Koob E
Abteilung für Plastische- und Handchirurgie St. Josef Hospitale in Essen-Kupferdreh.
Z Orthop Ihre Grenzgeb. 1993 Jul-Aug;131(4):340-3. doi: 10.1055/s-2008-1040036.
Melorheostosis is a rare monostotic or polyostotic bone disease of unknown etiology. It is characterized by a slowly progressing linear hyperostosis, fibrosis of the skin and subcutaneous tissues, contractures of joints and aching pain. The lower extremities are involved much more often than the upper extremities. The distribution of the lesion usually follows sclerotomes. Bone scanning complements standard radiologic studies and permits evaluation of the extent and activity of the disease. Here we report two cases of melorheostosis. Conservative treatment was disappointing. Thus we recommend the excision of the exostosis.
骨肥大症是一种病因不明的罕见单骨型或多骨型骨病。其特征为缓慢进展的线性骨质增生、皮肤及皮下组织纤维化、关节挛缩和疼痛。下肢受累比上肢更常见。病变分布通常沿皮节分布。骨扫描辅助标准放射学检查,可评估疾病的范围和活动度。我们在此报告两例骨肥大症病例。保守治疗效果不佳。因此我们建议切除骨疣。