Meilhac B, Fleury G, Caspi G, d'Arcy F F, Heulin A, Di Matteo J
Arch Mal Coeur Vaiss. 1976 May;69(5):547-52.
The authors report a case of Steinert's disease with disordered sino-atrial and atrio-ventricular conduction. The presence of sudden syncopal attacks and the absence of a cardiomyopathy (excluded by right- and leftsided haemodynamic studies and coronary arteriography) indicated the insertion of a definitive intra-cavitary pacemaker, especially as the life expectancy of this 54 year old patient did not seem to have been significantly reduced by his disease.
作者报告了一例伴有窦房和房室传导紊乱的斯坦纳特病病例。突发晕厥发作的存在以及心肌病的排除(通过左右心血流动力学研究和冠状动脉造影排除)表明需要植入永久性心腔内起搏器,特别是因为这位54岁患者的预期寿命似乎并未因疾病而显著缩短。