Komajda M, Frank R, Vedel J, Fontaine G, Petitot J C, Grosgogeat Y
Br Heart J. 1980 Mar;43(3):315-20. doi: 10.1136/hrt.43.3.315.
Twelve patients with dystrophia myotonica had cardiac electrphysiological study for conduction disturbances (five cases) or for syncope (seven cases). Conduction disturbances were found in each case, being intranodal in two cases, intra-Hisian in three cases, or diffuse in seven cases. These findings are in agreement with those previously reported, and may be related to the high incidence of sudden death in these patients. Pacemakers are advocated in symptomatic patients, and in some asymptomatic patients with severe and diffuse lesions.
12例强直性肌营养不良患者因传导障碍（5例）或晕厥（7例）接受了心脏电生理检查。所有病例均发现有传导障碍，其中2例为结内传导障碍，3例为希氏束内传导障碍，7例为弥漫性传导障碍。这些发现与先前报道的一致，可能与这些患者的猝死高发生率有关。对于有症状的患者以及一些有严重弥漫性病变的无症状患者，提倡植入起搏器。
