强直性肌营养不良症的心脏内传导缺陷。12例的电生理研究
Intracardiac conduction defects in dystrophia myotonica. Electrophysiological study of 12 cases.
作者信息
Komajda M, Frank R, Vedel J, Fontaine G, Petitot J C, Grosgogeat Y
出版信息
Br Heart J. 1980 Mar;43(3):315-20. doi: 10.1136/hrt.43.3.315.
Abstract
Twelve patients with dystrophia myotonica had cardiac electrphysiological study for conduction disturbances (five cases) or for syncope (seven cases). Conduction disturbances were found in each case, being intranodal in two cases, intra-Hisian in three cases, or diffuse in seven cases. These findings are in agreement with those previously reported, and may be related to the high incidence of sudden death in these patients. Pacemakers are advocated in symptomatic patients, and in some asymptomatic patients with severe and diffuse lesions.
摘要
12例强直性肌营养不良患者因传导障碍（5例）或晕厥（7例）接受了心脏电生理检查。所有病例均发现有传导障碍，其中2例为结内传导障碍，3例为希氏束内传导障碍，7例为弥漫性传导障碍。这些发现与先前报道的一致，可能与这些患者的猝死高发生率有关。对于有症状的患者以及一些有严重弥漫性病变的无症状患者，提倡植入起搏器。
相似文献
1
Intracardiac conduction defects in dystrophia myotonica. Electrophysiological study of 12 cases.强直性肌营养不良症的心脏内传导缺陷。12例的电生理研究
Br Heart J. 1980 Mar;43(3):315-20. doi: 10.1136/hrt.43.3.315.
2
Electrophysiological studies in two patients with dystrophia myotonica and atrioventricular conduction block.
Jpn Heart J. 1979 Jul;20(4):571-6. doi: 10.1536/ihj.20.571.
3
What is the best way to detect infra-Hisian conduction abnormalities and prevent sudden cardiac death in myotonic dystrophy?检测强直性肌营养不良中希氏束以下传导异常并预防心源性猝死的最佳方法是什么？
Heart. 2012 Mar;98(6):433-4. doi: 10.1136/heartjnl-2011-301407.
4
[Cardiac manifestations of dystrophia myotonica].[强直性肌营养不良的心脏表现]
Rev Clin Esp. 1975 Feb 15;136(3):235-41.
5
The natural course of cardiac conduction disturbances in myotonic dystrophy.强直性肌营养不良中心脏传导障碍的自然病程。
Cardiology. 1991;79(2):93-8. doi: 10.1159/000174865.
6
[Electrocardiography and electrophysiologic findings in patients with myotonic muscular dystrophy].
Z Kardiol. 1993 Aug;82(8):474-6.
7
Malignant cardiac involvement in a family with myotonic dystrophy.强直性肌营养不良家族中的恶性心脏受累情况。
G Ital Cardiol. 1996 Aug;26(8):853-61.
8
Pathology of the cardiac conduction system in myotonic dystrophy: a study of 12 cases.强直性肌营养不良症心脏传导系统的病理学：12例研究
J Am Coll Cardiol. 1988 Mar;11(3):662-71. doi: 10.1016/0735-1097(88)91547-1.
9
The evolution of infrahissian conduction time in myotonic dystrophy patients: clinical implications.肌强直性营养不良患者的下喉神经传导时间的演变：临床意义。
Heart. 2012 Feb;98(4):291-6. doi: 10.1136/heartjnl-2011-300143. Epub 2011 Oct 29.
10
Site of conduction disturbances in a family with myotonic dystrophy.
Am J Cardiol. 1973 Jul;32(1):114-8. doi: 10.1016/s0002-9149(73)80096-7.
引用本文的文献
1
Late Sodium Current Inhibitors as Potential Antiarrhythmic Agents.晚期钠电流抑制剂作为潜在的抗心律失常药物。
Front Pharmacol. 2020 Apr 20;11:413. doi: 10.3389/fphar.2020.00413. eCollection 2020.
2
Nonsustained ventricular tachycardia does not affect the prognosis of neuromuscular diseases: A preliminary and retrospective study.非持续性室性心动过速不影响神经肌肉疾病的预后：一项初步回顾性研究。
J Arrhythm. 2018 Apr 16;34(3):254-260. doi: 10.1002/joa3.12057. eCollection 2018 Jun.
3
Inhibition of Late Sodium Current as an Innovative Antiarrhythmic Strategy.抑制晚钠电流作为一种创新的抗心律失常策略。
Curr Heart Fail Rep. 2017 Jun;14(3):179-186. doi: 10.1007/s11897-017-0333-0.
4
Unmasked Brugada pattern by ajmaline challenge in patients with myotonic dystrophy type 1.1型强直性肌营养不良患者通过阿义马林激发试验揭示的Brugada波型
Ann Noninvasive Electrocardiol. 2015 Jan;20(1):28-36. doi: 10.1111/anec.12168. Epub 2014 Jun 18.
5
Is it possible to identify infrahissian cardiac conduction abnormalities in myotonic dystrophy by non-invasive methods?是否有可能通过非侵入性方法识别强直性肌营养不良患者的希氏束下心脏传导异常？
Heart. 1999 Nov;82(5):634-7. doi: 10.1136/hrt.82.5.634.
6
Electrocardiographic findings in myotonic dystrophy.强直性肌营养不良的心电图表现
Br Heart J. 1988 Jan;59(1):47-52. doi: 10.1136/hrt.59.1.47.
7
Myotonia dystrophica--first presentation as severe left ventricular failure complicating dilated cardiomyopathy.营养不良性肌强直——首次表现为严重左心室衰竭并发扩张型心肌病。
Postgrad Med J. 1992 Jan;68(795):67. doi: 10.1136/pgmj.68.795.67.
本文引用的文献
1
The heart in myotonia atrophica.萎缩性肌强直中的心脏
Br Heart J. 1951 Jul;13(3):343-7. doi: 10.1136/hrt.13.3.343.
2
Cardiovascular observations in dystrophia myotonica.强直性肌营养不良的心血管观察
J Am Med Assoc. 1950 Sep 23;144(4):299-303. doi: 10.1001/jama.1950.02920040013004.
3
THE HEART IN MYOTONIC DISEASE.
Acta Med Scand. 1964 Oct;176:479-91. doi: 10.1111/j.0954-6820.1964.tb00953.x.
4
MYOTONIC MUSCULAR DYSTROPHY; SYSTEMIC MANIFESTATIONS.强直性肌营养不良；全身表现
Arch Intern Med. 1964 Nov;114:669-79. doi: 10.1001/archinte.1964.03860110139016.
5
MYOTONIA DYSTROPHICA WITH A-V DISSOCIATION AND STOKES-ADAMS ATTACKS: A CASE REPORT AND REVIEW OF THE LITERATURE.伴有房室分离及斯托克斯－亚当斯发作的强直性肌营养不良：一例报告及文献复习
Am Heart J. 1964 Sep;68:391-6. doi: 10.1016/0002-8703(64)90307-2.
6
VECTORCARDIOGRAPHIC AND ELECTROCARDIOGRAPHIC FINDINGS IN MYOTONIA ATROPHICA. A STUDY EMPLOYING THE FRANK LEAD SYSTEM.萎缩性肌强直的向量心电图和心电图表现。一项采用弗兰克导联系统的研究。
Am Heart J. 1964 May;67:599-609. doi: 10.1016/0002-8703(64)90330-8.
7
A-V dissociation in dystrophia myotonica.强直性肌营养不良中的房室分离。
Br Heart J. 1953 Jul;15(3):357-9. doi: 10.1136/hrt.15.3.357.
8
The heart in myotonia atrophica.萎缩性肌强直中的心脏
Arch Intern Med. 1967 Feb;119(2):176-81.
9
Catheter technique for recording His bundle activity in man.用于记录人体希氏束活动的导管技术。
Circulation. 1969 Jan;39(1):13-8. doi: 10.1161/01.cir.39.1.13.
10
Dystrophia cordis myotonica studied by serial histology of the pacemaker and conducting system.通过对起搏器和传导系统进行连续组织学研究的强直性肌营养不良性心肌病。
J Pathol Bacteriol. 1968 Oct;96(2):285-95. doi: 10.1002/path.1700960205.
Zotero 插件