Suzuki K, Murakami Y, Mimori S
Department of Paediatric Cardiology, Sakakibara Heart Institute, Tokyo, Japan.
Br Heart J. 1993 Oct;70(4):386-90. doi: 10.1136/hrt.70.4.386.
A 13 year old girl with multiple arterial stenoses of unknown aetiology is described. At the age of seven months she was noted to have cardiomegaly and diminished left ventricular ejection fraction with no cardiac anomaly. Cardiac function gradually improved and her condition remained satisfactory until she was 11 years old when multiple lesions in the coronary, cerebral, and left brachial arteries were diagnosed. Histological examination of an endomyocardial biopsy specimen from the right ventricle showed hypertrophic muscles surrounded by abundant fibrous tissue. Percutaneous transluminal angioplasty of the right coronary stenoses led to complete occlusion.
本文描述了一名病因不明的患有多处动脉狭窄的13岁女孩。七个月大时，她被发现有心脏扩大和左心室射血分数降低，但无心脏异常。心脏功能逐渐改善，她的病情一直令人满意，直到11岁时，被诊断出冠状动脉、脑动脉和左肱动脉有多发性病变。右心室心内膜活检标本的组织学检查显示，肥厚的肌肉被大量纤维组织包围。对右冠状动脉狭窄进行经皮腔内血管成形术导致完全闭塞。
