Sartori P C, Enayat M S, Darbyshire P J
Department of Haematology, Birmingham Children's Hospital.
Pediatr Hematol Oncol. 1993 Jul-Sep;10(3):271-7. doi: 10.3109/08880019309029496.
We describe a child with recurrent microangiopathic haemolytic anemia (MAHA) and thrombocytopenia (TCP) who presented on the first day of life. Remission was maintained only by regular infusions of fresh frozen plasma (FFP). This case shows similarities with others described in the literature as examples of thrombotic thrombocytopenic purpura (TTP), although the absence of renal or neurological involvement distinguishes this disorder from classical TTP.
我们描述了一名患有复发性微血管病性溶血性贫血（MAHA）和血小板减少症（TCP）的患儿，其在出生第一天就出现了症状。仅通过定期输注新鲜冷冻血浆（FFP）维持缓解状态。该病例与文献中描述为血栓性血小板减少性紫癜（TTP）的其他病例相似，尽管没有肾脏或神经系统受累可将这种疾病与经典TTP区分开来。
