Watanabe K, Wakai S, Kumakura N, Kurosu A, Nagai M, Tsuchioka T, Fujiwara T
Department of Neurosurgery, Dokkyo University School of Medicine.
Noshuyo Byori. 1993;10(1):75-9.
The authors report a case of 6-month-old boy with cerebellar medulloblastoma associated with malignant rhabdoid tumor of the kidney, presenting with an abdominal mass, large head and projectile vomiting. Following removal of the renal tumor, the mass arising from the superior vermis about 6 cm in diameter was removed by a combined right occipital transtentorial and suboccipital approach. The patient had been well for 3 months after surgery followed by chemotherapy but died eventually of tumor recurrence in the abdomen. Reported cases of malignant rhabdoid tumor of the kidney associated with brain tumor are reviewed and its characteristics are discussed.
作者报告了一例6个月大的男孩,患有小脑髓母细胞瘤并伴有肾恶性横纹肌样瘤,表现为腹部肿块、大头和喷射性呕吐。在切除肾肿瘤后,通过右枕下入路联合经小脑幕入路切除了起源于上蚓部直径约6厘米的肿块。患者术后化疗后情况良好3个月,但最终死于腹部肿瘤复发。本文回顾了已报道的肾恶性横纹肌样瘤合并脑肿瘤的病例,并讨论了其特征。