Komori H, Matsuishi T, Abe T, Nagata Y, Ohtaki E, Kojima K, Yukizane S
Department of Pediatrics and Child Health, Kurume University School of Medicine, Japan.
J Child Neurol. 1993 Oct;8(4):412-5. doi: 10.1177/088307389300800423.
A 2-year-old girl with Turner syndrome was admitted with left hemiplegia and left facial palsy. Serial cranial computed tomographic scan demonstrated multiple cerebral infarctions in the right putamen and right medial cortical areas. Single photon emission computed tomographic scan revealed hypoperfusion from the right frontal to the right temporal area. Right carotid angiography showed narrowing and occlusion of the right internal carotid artery at the sphenoidal portion. Collateral circulation was not detected between the external and internal carotid arteries. Left carotid angiography revealed that the left anterior artery was narrow, and that the left internal carotid artery provided blood to the right internal carotid artery through the anterior communicating artery. These findings suggested that the cerebrovascular abnormality might be due to congenital hypoplasia of arteries in this patient. The unusual combination of cerebral infarction and Turner syndrome was reported.
一名患有特纳综合征的2岁女孩因左侧偏瘫和左面神经麻痹入院。系列头颅计算机断层扫描显示右侧壳核和右侧内侧皮质区域有多处脑梗死。单光子发射计算机断层扫描显示从右侧额叶到右侧颞叶区域灌注不足。右侧颈动脉血管造影显示右侧颈内动脉蝶骨段狭窄和闭塞。未检测到颈外动脉和颈内动脉之间的侧支循环。左侧颈动脉血管造影显示左侧前动脉狭窄，左侧颈内动脉通过前交通动脉向右侧颈内动脉供血。这些发现提示该患者的脑血管异常可能是由于动脉先天性发育不全所致。本文报道了脑梗死与特纳综合征的不寻常组合。
