Tai C C, Lee P, Wood R E
Department of Dentistry, Ontario Cancer Institute incorporating Princess Margaret Hospital, Canada.
Pediatr Dent. 1993 Jul-Aug;15(4):275-9.
A case of pediatric progressive systemic sclerosis is reported and a literature review concerning medical and dental aspects of this condition is provided. Systemic features include sclerodactyly, Raynaud's phenomenon, telangiectasia, calcinosis, myositis, arthritis, tenosynovitis, renal failure, esophageal hypomotility, pulmonary fibrosis and heart failure. Oral manifestations include reduced interincisal distance, xerostomia, telangiectasia, increased periodontal ligament width, osseous resorption of the mandible, periodontal disease, and increased decayed, missing, and filled teeth (DMFT). The prognosis is difficult to predict because spontaneous remission has been documented, but death may result from extensive visceral involvement (heart, kidney, and lung).
报告了一例儿童进行性系统性硬化症病例，并提供了有关该疾病医学和牙科方面的文献综述。全身症状包括指（趾）硬化、雷诺现象、毛细血管扩张、钙质沉着、肌炎、关节炎、腱鞘炎、肾衰竭、食管动力不足、肺纤维化和心力衰竭。口腔表现包括切牙间距离减小、口干、毛细血管扩张、牙周膜增宽、下颌骨骨质吸收、牙周病以及龋失补牙数（DMFT）增加。由于已有自发缓解的记录，所以预后难以预测，但广泛的内脏受累（心脏、肾脏和肺部）可能导致死亡。
