Zimmermann R, Huch A
Department of Obstetrics, University of Zurich, Switzerland.
Fetal Diagn Ther. 1993 Jul-Aug;8(4):268-72. doi: 10.1159/000263838.
A large contained urinoma measuring 12 x 8 x 8 cm3 was diagnosed in the left kidney of a female fetus at 28 weeks gestation. Analysis of fluid from serial punctures of the cyst indicated that renal function on that side was poor, but because ultrasound findings of the thorax suggested lung growth impairment, a shunt was inserted. After 3 weeks the shunt dislocated into the fetal abdominal cavity and urinous ascites developed. The ascites was found to have resolved spontaneously on ultrasonography 3 weeks later. The infant was delivered at 37 weeks gestation and appeared normal except for bilateral pelvi-ureteric obstruction. This was much worse in the left kidney, the renal function of which was only 10% of normal. A left nephrectomy was carried out when the infant was 6 months old, when the inner part of the shunt was discovered in perinephric fibrous tissue. The renal pelvis was greatly enlarged and fibrotic; no site of rupture could be identified. The infant's respiratory function was normal. This case suggests the use of intrauterine shunting to decompress a large unilateral urinoma resulting in marked elevation of the fetal diaphragm to prevent impairment of fetal lung growth.
在一名妊娠28周的女性胎儿左肾中诊断出一个大小为12×8×8 cm³的巨大包裹性尿囊肿。对囊肿进行系列穿刺抽取的液体分析表明,患侧肾功能较差,但由于胸部超声检查结果提示肺部生长受限,于是插入了分流管。3周后,分流管移位至胎儿腹腔,出现了尿性腹水。3周后超声检查发现腹水已自行消退。该婴儿在妊娠37周时分娩,除双侧肾盂输尿管梗阻外,外观正常。左肾情况更糟,其肾功能仅为正常的10%。婴儿6个月大时进行了左肾切除术,此时在肾周纤维组织中发现了分流管的内部部分。肾盂明显增大且纤维化;未发现破裂部位。婴儿的呼吸功能正常。该病例提示,对于导致胎儿膈肌明显抬高的巨大单侧尿囊肿,可采用宫内分流术进行减压,以防止胎儿肺生长受限。