Young C A, MacKenzie J M, Chadwick D W, Williams I R
Walton Centre for Neurology and Neurosurgery, Liverpool, United Kingdom.
Eur J Med. 1993 Apr;2(4):239-41.
Opsoclonus-myoclonus is a rare clinical syndrome. We report three patients who died with a pure opsoclonus-myoclonus syndrome. The presentation, management and associations of this distinctive condition are discussed, and the results of detailed pathological examination described. In each case the only abnormality was perivascular collections of lymphocytes widely distributed in the brain. This supports an immune-mediated rather than structural aetiology.
眼阵挛-肌阵挛是一种罕见的临床综合征。我们报告了三例死于单纯眼阵挛-肌阵挛综合征的患者。本文讨论了这种独特病症的临床表现、治疗及相关情况,并描述了详细病理检查的结果。在每例病例中,唯一的异常是淋巴细胞在脑内广泛分布于血管周围。这支持了免疫介导而非结构性病因的观点。