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眼阵挛-肌阵挛综合征:三例尸检研究

Opsoclonus-myoclonus syndrome: an autopsy study of three cases.

作者信息

Young C A, MacKenzie J M, Chadwick D W, Williams I R

机构信息

Walton Centre for Neurology and Neurosurgery, Liverpool, United Kingdom.

出版信息

Eur J Med. 1993 Apr;2(4):239-41.

PMID:8261078
Abstract

Opsoclonus-myoclonus is a rare clinical syndrome. We report three patients who died with a pure opsoclonus-myoclonus syndrome. The presentation, management and associations of this distinctive condition are discussed, and the results of detailed pathological examination described. In each case the only abnormality was perivascular collections of lymphocytes widely distributed in the brain. This supports an immune-mediated rather than structural aetiology.

摘要

眼阵挛-肌阵挛是一种罕见的临床综合征。我们报告了三例死于单纯眼阵挛-肌阵挛综合征的患者。本文讨论了这种独特病症的临床表现、治疗及相关情况,并描述了详细病理检查的结果。在每例病例中,唯一的异常是淋巴细胞在脑内广泛分布于血管周围。这支持了免疫介导而非结构性病因的观点。

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1
Opsoclonus-myoclonus syndrome: an autopsy study of three cases.眼阵挛-肌阵挛综合征:三例尸检研究
Eur J Med. 1993 Apr;2(4):239-41.
2
[A case of opsoclonus-myoclonus syndrome associated with anti-central nervous system antibody].
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Myasthenia gravis in a child with sequelae of opsoclonus-myoclonus syndrome.
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[Opsoclonus-myoclonus syndrome in the adult. 4 cases].
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引用本文的文献

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Immune-Mediated Cerebellar Ataxias: Clinical Diagnosis and Treatment Based on Immunological and Physiological Mechanisms.免疫介导的小脑性共济失调:基于免疫和生理机制的临床诊断与治疗
J Mov Disord. 2021 Jan;14(1):10-28. doi: 10.14802/jmd.20040. Epub 2021 Jan 12.
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Immune-mediated Cerebellar Ataxias: Practical Guidelines and Therapeutic Challenges.免疫介导的小脑共济失调:实用指南与治疗挑战。
Curr Neuropharmacol. 2019;17(1):33-58. doi: 10.2174/1570159X16666180917105033.
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Clinical and Immunological Features of Opsoclonus-Myoclonus Syndrome in the Era of Neuronal Cell Surface Antibodies.
神经元细胞表面抗体时代下斜视性眼阵挛-肌阵挛综合征的临床与免疫学特征
JAMA Neurol. 2016 Apr;73(4):417-24. doi: 10.1001/jamaneurol.2015.4607.