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The role of glycosidically bound mannose in the assimilation of beta-galactosidase by generalized gangliosidosis fibroblasts.

作者信息

Hieber V, Distler J, Myerowitz R, Schmickel R D, Jourdian G W

出版信息

Biochem Biophys Res Commun. 1976 Dec 6;73(3):710-7. doi: 10.1016/0006-291x(76)90868-8.

DOI:10.1016/0006-291x(76)90868-8
PMID:827294
Abstract
摘要

相似文献

1
The role of glycosidically bound mannose in the assimilation of beta-galactosidase by generalized gangliosidosis fibroblasts.糖苷键结合甘露糖在全身性神经节苷脂沉积症成纤维细胞对β-半乳糖苷酶的同化作用中的作用。
Biochem Biophys Res Commun. 1976 Dec 6;73(3):710-7. doi: 10.1016/0006-291x(76)90868-8.
2
Selective noncompetitive assimilation of bovine testicular beta-galactosidase and bovine liver beta-glucuronidase by generalized gangliosidosis fibroblasts.全身性神经节苷脂沉积症成纤维细胞对牛睾丸β-半乳糖苷酶和牛肝β-葡萄糖醛酸酶的选择性非竞争性同化作用
J Clin Invest. 1980 Apr;65(4):879-84. doi: 10.1172/JCI109740.
3
Binding of human liver beta-galactosidases to plant lectins insolubilized on agarose.人肝脏β-半乳糖苷酶与固定在琼脂糖上的植物凝集素的结合。
Biochem Biophys Res Commun. 1974 Jan;56(1):193-8. doi: 10.1016/s0006-291x(74)80333-5.
4
Atypical adult GM1 gangliosidosis: biochemical comparison with other forms of primary beta-galactosidase deficiency.非典型成人GM1神经节苷脂贮积症：与其他形式原发性β-半乳糖苷酶缺乏症的生化比较
Neurology. 1986 Sep;36(9):1237-41. doi: 10.1212/wnl.36.9.1237.
5
Effects of exogenous beta-galactosidase on cultured fibroblasts with beta-galactosidase deficiency.外源性β-半乳糖苷酶对β-半乳糖苷酶缺乏的培养成纤维细胞的影响。
Clin Chim Acta. 1987 Apr 15;164(1):101-7. doi: 10.1016/0009-8981(87)90111-2.
6
Correction of accumulation of sulfate-containing compounds in cultured generalized gangliosidosis fibroblasts by beta-galactosidase.β-半乳糖苷酶对培养的全身性神经节苷脂沉积症成纤维细胞中含硫酸盐化合物蓄积的纠正作用
Birth Defects Orig Artic Ser. 1975;11(6):311-5.
7
Purification of N-acetyl D-glucosamine-binding proteins by affinity chromatography.通过亲和色谱法纯化N-乙酰-D-葡萄糖胺结合蛋白。
FEBS Lett. 1974 Mar 15;40(1):62-6. doi: 10.1016/0014-5793(74)80894-x.
8
A case of GM1-gangliosidosis type I: glycosphingolipid profiles of urine and transformed lymphocytes and beta-D-galactosidase activities in peripheral lymphocytes, cultured skin fibroblasts and transformed lymphocytes.I型GM1神经节苷脂贮积症一例：尿液、转化淋巴细胞的糖鞘脂谱以及外周淋巴细胞、培养的皮肤成纤维细胞和转化淋巴细胞中的β-D-半乳糖苷酶活性
Jpn J Exp Med. 1990 Apr;60(2):73-9.
9
Prenatal diagnosis of GM1-gangliosidosis: biochemical manifestations in fetal tissues.GM1神经节苷脂贮积症的产前诊断：胎儿组织中的生化表现
Hum Genet. 1978 Nov 16;44(3):287-93. doi: 10.1007/BF00394293.
10
Enhanced proteolytic degradation of normal beta-galactosidase in the lysosomal storage disease with combined beta-galactosidase and neuraminidase deficiency.在伴有β-半乳糖苷酶和神经氨酸酶联合缺乏的溶酶体贮积病中，正常β-半乳糖苷酶的蛋白水解降解增强。
Biochim Biophys Acta. 1982 Apr 21;703(1):69-76. doi: 10.1016/0167-4838(82)90012-7.

引用本文的文献

1
Biochemical composition and changes of extracellular polysaccharides (ECPS) produced during microphytobenthic biofilm development (Marennes-Oléron, France).微藻生物膜发育过程中胞外多糖（ECPS）的生化组成及其变化（法国马伦内奥勒隆）。
Microb Ecol. 2012 Jan;63(1):157-69. doi: 10.1007/s00248-011-9959-8. Epub 2011 Oct 15.
2
Fibroblast receptor for lysosomal enzymes mediates pinocytosis of multivalent phosphomannan fragment.溶酶体酶的成纤维细胞受体介导多价磷酸甘露聚糖片段的胞饮作用。
J Cell Biol. 1980 Jan;84(1):77-86. doi: 10.1083/jcb.84.1.77.
3
Selective noncompetitive assimilation of bovine testicular beta-galactosidase and bovine liver beta-glucuronidase by generalized gangliosidosis fibroblasts.
全身性神经节苷脂沉积症成纤维细胞对牛睾丸β-半乳糖苷酶和牛肝β-葡萄糖醛酸酶的选择性非竞争性同化作用
J Clin Invest. 1980 Apr;65(4):879-84. doi: 10.1172/JCI109740.
4
Subcellular distribution of acid alpha-glucosidase in fibroblasts and of antigenically cross-reactive material in Pompe's disease fibroblasts.成纤维细胞中酸性α-葡萄糖苷酶的亚细胞分布以及庞贝病成纤维细胞中抗原交叉反应物质的亚细胞分布。
Histochem J. 1986 Nov-Dec;18(11-12):613-24. doi: 10.1007/BF01675297.
5
Phosphohexosyl recognition is a general characteristic of pinocytosis of lysosomal glycosidases by human fibroblasts.磷酸己糖识别是人类成纤维细胞对溶酶体糖苷酶进行胞饮作用的一个普遍特征。
J Clin Invest. 1977 Nov;60(5):1088-93. doi: 10.1172/JCI108860.
6
Secretion of beta-N-acetylglucosaminidase isoenzymes by normal human fibroblasts.正常人成纤维细胞分泌β-N-乙酰氨基葡萄糖苷酶同工酶。
Biochem J. 1978 Aug 1;173(2):433-9. doi: 10.1042/bj1730433.
7
Evidence for lysosomal enzyme recognition by human fibroblasts via a phosphorylated carbohydrate moiety.人类成纤维细胞通过磷酸化碳水化合物部分识别溶酶体酶的证据。
Biochem J. 1978 Mar 15;170(3):643-50. doi: 10.1042/bj1700643.
8
Enzymatic identification of mannose 6-phosphate on the recognition marker for receptor-mediated pinocytosis of beta-glucuronidase by human fibroblasts.人成纤维细胞对β-葡萄糖醛酸酶进行受体介导的胞吞作用的识别标记物上磷酸甘露糖的酶促鉴定。
Proc Natl Acad Sci U S A. 1979 Sep;76(9):4322-6. doi: 10.1073/pnas.76.9.4322.
9
Direct demonstration of binding of a lysosomal enzyme, alpha-L-iduronidase, to receptors on cultured fibroblasts.溶酶体酶α-L-艾杜糖醛酸酶与培养的成纤维细胞上受体结合的直接证明。
Proc Natl Acad Sci U S A. 1979 May;76(5):2331-4. doi: 10.1073/pnas.76.5.2331.
10
Phosphohexosyl components of a lysosomal enzyme are recognized by pinocytosis receptors on human fibroblasts.
Proc Natl Acad Sci U S A. 1977 May;74(5):2026-30. doi: 10.1073/pnas.74.5.2026.