Lhotta K, Kronenberg F, Joannidis M, Feichtinger H, König P
Dept. of Internal Medicine, Innsbruck University Hospital, Austria.
Adv Exp Med Biol. 1993;336:415-8. doi: 10.1007/978-1-4757-9182-2_72.
Described here is a family in which the father with partial C4 deficiency had Wegener's granulomatosis and a son with complete C4 deficiency presented with Henoch-Schönlein Purpura. The possible role of C4 deficiency in the pathogenesis of both vasculitic disorders is discussed.
