Ragosta K
Department of Pediatrics, State University of New York, Syracuse.
Clin Pediatr (Phila). 1993 Nov;32(11):685-7. doi: 10.1177/000992289303201109.
Miller Fisher syndrome is a rare focal encephalitis of the brainstem characterized by cranial nerve palsy, ataxia, and areflexia. While this condition usually is mild and self-limiting, as this case documents, findings may fulfill many of the criteria in the clinical examination for brain death. Unlike brain death, however, it is not associated with irreparable structural damage of the brain or, as is mandatory, does it fulfill a very important prerequisite of brain death, the exclusion of potentially reversible causes of coma. Treatment of Miller Fisher syndrome is supportive.
米勒-费雪综合征是一种罕见的脑干局灶性脑炎，其特征为颅神经麻痹、共济失调和腱反射消失。虽然这种病症通常症状较轻且具有自限性，但正如本病例所记录的那样，其检查结果可能符合脑死亡临床检查中的许多标准。然而，与脑死亡不同的是，它与大脑的不可修复性结构损伤无关，而且它也不符合脑死亡的一个非常重要的先决条件，即排除昏迷的潜在可逆原因。米勒-费雪综合征的治疗以支持治疗为主。
