Tamaki S, Ito T, Takagi Y, Ichihara T, Kajiyama M, Mizuno S, Tanaka M, Abe T
Department of Thoracic Surgery, School of Medicine Nagoya University, Japan.
Kyobu Geka. 1994 Feb;47(2):115-8.
A 20-year-old man with Marfan syndrome was recommended emergency operation for impending rupture of TAA. Because he was in the state of acute heart failure due to coexisting AAE and AR, so the simultaneous operations for AAE, AR and TAA were needed. He underwent Bentall, arch replacement and elephant trunk operation utilizing separate extracorporeal circulation and circulatory arrest. Chest CT, taken after 5 months postoperatively, revealed only a small amount of thrombus in TAA. Anticoagulation therapy stood in the way of aneurysmal thrombo-exclusion. The second operation, grafting of descending thoracic aorta, was performed 6 months later and elephant trunk made the second operation easier. Now 12 months passed after the second operation, he is in good health.
一名患有马凡综合征的20岁男性因胸主动脉瘤（TAA）即将破裂而被建议进行急诊手术。由于他同时存在主动脉瓣反流（AAE）和主动脉反流（AR），处于急性心力衰竭状态，因此需要同时进行AAE、AR和TAA手术。他接受了Bentall手术、主动脉弓置换术和象鼻手术，采用了单独的体外循环和循环停止技术。术后5个月的胸部CT显示TAA内仅有少量血栓。抗凝治疗妨碍了动脉瘤血栓排除。6个月后进行了第二次手术，即胸降主动脉移植术，象鼻技术使第二次手术更容易进行。现在第二次手术后已经过去了12个月，他身体健康。
