Ceddia A, Di Rocco C, Carlucci A
Istituto di Neurochirurgia, Policlinico A. Gemelli, UCSC, Roma.
Minerva Pediatr. 1993 Sep;45(9):363-7.
The authors present a case of a nine month-old baby with hypersecretive congenital hydrocephalus. The CSF overproduction was the result of a rare abnormality of the choroid plexus, a villous hypertrophy of the right ventricular choroid plexus and a left ventricular plexus papilloma. Surgical removal of the plexus papilloma and the plexectomy of the hypertrophic ventricular structure did not ameliorate the hydrocephalus, which has been controlled after a biventricular-peritoneal shunt. The physiopathological relationship between hydrocephalus and choroid plexus abnormalities are reported. The importance of an early diagnosis and treatment is stressed. Both hydrocephalus and choroid plexus pathology may represent a cause of psychomotor delay, for the little patient the effects of which is investigated in this paper.
作者报告了一例9个月大患有分泌过多性先天性脑积水的婴儿病例。脑脊液分泌过多是由脉络丛罕见异常所致，即右心室脉络丛绒毛样肥大及左心室丛状乳头状瘤。手术切除丛状乳头状瘤及对肥厚的脑室结构进行脉络丛切除术并未改善脑积水情况，在进行双侧脑室 - 腹腔分流术后脑积水得到控制。本文报告了脑积水与脉络丛异常之间的生理病理关系。强调了早期诊断和治疗的重要性。脑积水和脉络丛病变均可能是精神运动发育迟缓的原因，本文对该患儿所受影响进行了研究。
