Brietta L K, Watkins D
Department of Pathology, Baylor University Medical Center, Dallas, Tex. 75246.
Arch Pathol Lab Med. 1994 Feb;118(2):188-90.
Myelolipomas are rare, benign tumors composed in varying proportions of adipose tissue and hematopoietic cells. Myelolipomas are typically found in the adrenal gland, but uncommon cases of extra-adrenal sites have been reported, primarily presacrally. Extra-adrenal myelolipomas must be distinguished from masses of extramedullary hematopoiesis, which are also composed of hematopoietic elements but are associated with anemia and marked bone marrow hyperplasia. Also, if the distinction between extra-adrenal myelolipomas and malignant tumors such as liposarcoma were made before surgery, an invasive procedure might be avoided. We report the case of an extremely large, asymptomatic, perirenal myelolipoma in a 66-year-old diabetic woman. We also review the literature on extra-adrenal myelolipomas.
肾上腺髓质脂肪瘤是一种罕见的良性肿瘤，由不同比例的脂肪组织和造血细胞组成。肾上腺髓质脂肪瘤通常见于肾上腺，但也有罕见的肾上腺外部位的病例报道，主要位于骶前。肾上腺外髓质脂肪瘤必须与髓外造血肿块相鉴别，后者也由造血成分组成，但与贫血和明显的骨髓增生有关。此外，如果在手术前能够区分肾上腺外髓质脂肪瘤和恶性肿瘤如脂肪肉瘤，就可以避免采用侵入性手术。我们报告了一例66岁糖尿病女性患者患有一个巨大、无症状的肾周髓质脂肪瘤的病例。我们还回顾了有关肾上腺外髓质脂肪瘤的文献。
