Brachet A, Thévenet F, Gilly F N, Trillet-Lenoir V, Tabib A Z, Brune J, Loire R, Gamondes J P
Clinique Chirurgicale-B, Hôpital Lyon-Sud, Pierre-Benite.
Ann Chir. 1993;47(2):170-3.
The patient reported here had no particular past history. He presented with effort dyspnea, jugular turgescence and positional vertigo suggestive of a superior vena cava obstruction syndrome. Bronchial fibroscopy was normal, but chest X-ray, CT scan and phlebography of the superior vena cava revealed an anterior mediastinal tumour compressing the superior vena cava. The tumour was excised with replacement of the vena cava by a PTFE n. 16 graft. Pathological examination showed this to be an inflammatory tumour by fibrosis with plasmocytes. This plasmocyte fibrosis is histologically benign and becomes malignant only when complications occur as a result of its spread.
本文报告的患者既往无特殊病史。他表现为劳力性呼吸困难、颈静脉怒张和体位性眩晕,提示上腔静脉阻塞综合征。支气管纤维镜检查正常,但胸部X线、CT扫描及上腔静脉静脉造影显示前纵隔肿瘤压迫上腔静脉。肿瘤被切除,并用16号聚四氟乙烯移植物置换上腔静脉。病理检查显示这是一种伴有浆细胞的纤维化炎症性肿瘤。这种浆细胞纤维化在组织学上是良性的,只有当因扩散而出现并发症时才会恶变。