Anomalies of the intrahepatic portal venous system in congenital hepatic fibrosis.

Duplication of intrahepatic venous channels was observed in 9 of 13 children with congenital hepatic fibrosis and portal hypertension. Portal hypertension due to other causes was not associated with venous duplication. This anomaly may be a distinctive feature of congenital hepatic fibrosis with portal hypertension.