Kuhn W
Schweiz Med Wochenschr. 1977 Feb 5;107(5):138-44.
A case is reported of angiosarcoma occuring in the chronic-lymphedematous right arm of a 56 year-old woman 9 years after radical mastectomy for cancer of the right breast. This is a characteristic example of Stewart-Treves syndrome (angiosarcoma in chronic lymphedema). The patient died within the year from multiple metastases. About 200 such cases are reported in the literature: the prognosis is bad, the best therapy reported being amputation of the extremity. Early diagnosis is essential through frequent checks for chronic lymphedema, which is seemingly the crucial etiologic factor in the occurrence of this angiosarcoma. Histogenesis has yet to be fully explained.
报告了一例血管肉瘤病例,发生在一名56岁女性的慢性淋巴水肿右臂,该患者9年前因右乳腺癌行根治性乳房切除术。这是斯图尔特 - 特里夫斯综合征(慢性淋巴水肿中的血管肉瘤)的典型病例。患者在一年内死于多处转移。文献中报道了约200例此类病例:预后不良,据报道最佳治疗方法是截肢。通过对慢性淋巴水肿进行频繁检查以实现早期诊断至关重要,慢性淋巴水肿似乎是这种血管肉瘤发生的关键病因。组织发生学尚未得到充分解释。