Stoba C, Skoczylas-Stoba B, Czauderna P
Clinic of Pediatric Surgery, Medical Academy, Gdańsk, Poland.
Eur J Pediatr Surg. 1993 Jun;3(3):154-6. doi: 10.1055/s-2008-1063532.
Between 1965 and 1990 five children with pheochromocytomas were treated. Clinical course, methods of diagnosis, treatment and results established by follow-up from 6 months to 20 years are presented. Hypertension and headaches occurred in all patients. One child with a malignant form of pheochromocytoma manifested central nervous symptoms imitating epilepsy and additionally diffuse pulmonary metastases were found. One patient had a family history of pheochromocytomas and presented with hypermetabolic state and neurovegetative symptoms. One child had multifocal tumors: two in the posterior mediastinum and one in the retroperitoneal space. All patients were treated by either enucleation of the tumor, tumor excision or adrenalectomy. One child died 12 years after surgery from the rapid progression of pulmonary metastases of pheochromoblastoma present at the time of diagnosis.
1965年至1990年间，对5例嗜铬细胞瘤患儿进行了治疗。本文介绍了临床病程、诊断方法、治疗方法以及随访6个月至20年的结果。所有患者均出现高血压和头痛症状。1例患有恶性嗜铬细胞瘤的患儿表现出类似癫痫的中枢神经系统症状，此外还发现有弥漫性肺转移。1例患者有嗜铬细胞瘤家族史，表现为高代谢状态和植物神经症状。1例患儿有多发性肿瘤：后纵隔有2个，腹膜后间隙有1个。所有患者均接受了肿瘤剜除术、肿瘤切除术或肾上腺切除术。1例患儿在手术后12年因诊断时就已存在的嗜铬细胞瘤肺转移迅速进展而死亡。
