Olgun N, Oren H, Oren B, Irken G, Polat M, Cevik N
Department of Pediatrics, Faculty of Medicine, Dokuz Eylül University, Izmir, Turkey.
Dermatology. 1993;187(2):127-9. doi: 10.1159/000247222.
We report a case of diffuse erythrodermic cutaneous mastocytosis with bone marrow infiltration. An 11-month-old female patient was referred to our hospital for intermittent flushing, fever, intense itching, erythematous rash and bullous lesions. Cutaneous biopsy demonstrated diffuse cutaneous mastocytosis. The bone marrow aspirate revealed mast cell infiltration. Ketotifen treatment was very effective.
我们报告一例伴有骨髓浸润的弥漫性红皮病型皮肤肥大细胞增多症。一名11个月大的女性患者因间歇性潮红、发热、剧烈瘙痒、红斑皮疹和水疱性病变被转诊至我院。皮肤活检显示为弥漫性皮肤肥大细胞增多症。骨髓穿刺显示有肥大细胞浸润。酮替芬治疗非常有效。