Hsiao Y C, Chen C C, Shih T Y, Shih H S, Chen W, Wu N K
Department of Pediatrics, Taipei Municipal Chung-Hsiao Hospital, Taiwan, R.O.C.
Zhonghua Min Guo Xiao Er Ke Yi Xue Hui Za Zhi. 1993 Mar-Apr;34(2):151-6.
A five-year-old girl had been noted, since birth to have abdominal distension. There was no history of twinning or teratoma in the family. Physical examination discovered a 15 x 10 cm mass in the abdomen. Roentgenologic examination demonstrated the presence of an axial skeleton and long bones within the mass. MRI showed a retroperitoneal mass with components of cystic, bony and fatty tissues. When the mass was surgically removed from the retroperitoneal cavity, pathologic examination disclosed a parasitic fetus measuring 15.3 x 6.3 x 6.0 cm in size and suspended by a peduncle within a capsule. The fetus was covered with skin, sebaceous materials and black hair. There were bilateral and symmetric upper extremities with a flapper-like, deformed hand. No obvious genital organ was noted. Dissection of the midline, revealed a vertebral column with spinal cord. An atrophic skull bone containing cephalized glial tissue was noted. A thoracic cavity and scapular bone were found in the thoracic cage; however, no heart was noted. Gastrointestinal tract and kidney-like organs were seen within the abdominal cavity. Microscopically, there were glial tissues within the skull bone, spinal cord and vertebra. The upper extremities revealed two long bones surrounded by myxomatous and fibrous tissue. A well developed intestine and an ovary containing follicles with nearby lympy nodes were seen. The capsule showed fibrous tissue with calcification and hairs. It was distinguished from the teratoma by the presence of a vertebral axis and by an appropriate arrangement of other organs or limbs with respect to the axis, and corresponding to the generally recognized diagnostic criteria of fetus in fetu.
一名五岁女孩自出生起就被发现有腹部膨隆。家族中无双胎或畸胎瘤病史。体格检查发现腹部有一个15×10厘米的肿块。X线检查显示肿块内有中轴骨骼和长骨。磁共振成像（MRI）显示一个腹膜后肿块，包含囊性、骨性和脂肪性组织成分。当从腹膜后腔手术切除该肿块时，病理检查发现一个寄生胎，大小为15.3×6.3×6.0厘米，通过一个蒂悬吊在一个囊内。该胎儿覆盖着皮肤、皮脂物质和黑色毛发。有双侧对称的上肢，手部呈翼状畸形。未发现明显的生殖器官。沿中线切开，可见一个带有脊髓的脊柱。发现一个萎缩的颅骨，其中含有脑化的胶质组织。在胸廓内发现一个胸腔和肩胛骨；然而，未发现心脏。在腹腔内可见胃肠道和类似肾脏的器官。显微镜下，颅骨、脊髓和椎骨内有胶质组织。上肢可见两根长骨，周围有黏液瘤样和纤维组织。可见一段发育良好的肠管和一个含有卵泡的卵巢，附近有淋巴结。囊显示为有钙化和毛发的纤维组织。它与畸胎瘤的区别在于存在一个椎骨轴，以及其他器官或肢体相对于该轴的适当排列，符合胎内胎的一般公认诊断标准。
