Paume P, Grippari J L, Payement G, Dandrau J P, Cariou J L, Bellavoir A
Service de Chirurgie Plastique, H.I.A. Bégin, Saint-Mandé.
Rev Stomatol Chir Maxillofac. 1993;94(2):104-9.
A 19 year old girl presented with a dedifferentiated chondrosarcoma of maxilla. The recurring tumor, diagnosed initially from the provoked pain, appeared on the scan image as a heterogeneous mass containing numerous calcifications. Histology showed, within a well differentiated chondrosarcoma, an anaplastic sarcomatous zone of the malignant fibrous histiocytoma (MFH) type. This histologic appearance is consistent with a poorer clinical prognosis. Radical surgery of the 4th tumor recurrence was combined with maxillofacial prosthetic rehabilitation. This appears to be first reported case of a dedifferentiated chondrosarcoma of the MFH type located in the maxilla.
