一名27岁男性左心房复发性恶性纤维组织细胞瘤。

Recurrent malignant fibrous histiocytoma of the left atrium in a 27-year-old male.

作者信息

Wahba A, Liebold A, Birnbaum D E

机构信息

Department of Cardiac, Thoracic and Vascular Surgery, University Hospital, University of Regensburg, Germany.

出版信息

Eur J Cardiothorac Surg. 1993;7(7):387-9. doi: 10.1016/1010-7940(93)90072-j.

DOI:10.1016/1010-7940(93)90072-j

PMID:8396952

Abstract

We report a case of recurrent malignant fibrous histiocytoma (MFH) of the left atrium. The primary lesion was surgically removed after it had been diagnosed to be the cause of fulminant pulmonary edema in a 27-year-old male. The tumor recurred 15 weeks following surgery. It was excised completely, leaving a large left atrial defect that was reconstructed using a Dacron patch. Malignant fibrous histiocytoma constitutes 2% of all cardiac malignancies. The typical location is the left atrium. Surgical excision is the primary aim in treating this tumor. Adjuvant radiotherapy and chemotherapy have been suggested in the literature. The prognosis is poor.

摘要

我们报告一例左心房复发性恶性纤维组织细胞瘤（MFH）。一名27岁男性患者因暴发性肺水肿被诊断为由原发性病变引起，该原发性病变经手术切除。肿瘤在术后15周复发。再次将其完全切除，留下一个大的左心房缺损，使用涤纶补片进行重建。恶性纤维组织细胞瘤占所有心脏恶性肿瘤的2%。典型部位是左心房。手术切除是治疗该肿瘤的主要目的。文献中已建议辅助放疗和化疗。预后较差。