Thron A
Med Klin. 1977 Feb 11;72(6):199-203.
A case of a patient with multiple bilateral hamartomas of the kidneys is reported. The diagnosis of polycystic renal disease, suggested by the urographic studies had to be corrected after renal angiography. A well established diagnosis, basing on the striking angiographical findings was only possible, when we took notice of an adenoma sebaceum and other signs of the tuberous sclerosis complex. In cases of circumscribed unifocal lesions the antiographic findings may cause difficulties in the differential diagnosis between hamartoma and malignant hypernephroma. Therefore it is important to pay attention to other stigmata of tuberous sclerosis (Bourneville-Pringle's-syndrome). The differentiation between benign hamartoma and malignant hypernephroma may be possible by angiographic criteria alone, but many of the reported typical signs are of limited value.
报告了一例患有双侧多发性肾错构瘤的患者。静脉尿路造影检查提示为多囊肾疾病，但肾血管造影后该诊断必须修正。只有当我们注意到皮脂腺瘤和结节性硬化症复合体的其他体征时，基于显著的血管造影表现才能做出明确诊断。在局限性单发病变的病例中，血管造影结果可能会给错构瘤与恶性肾细胞瘤的鉴别诊断带来困难。因此，注意结节性硬化症（布尔内维尔-普林格尔综合征）的其他体征很重要。仅凭血管造影标准可能无法区分良性错构瘤和恶性肾细胞瘤，但许多已报道的典型体征价值有限。
