Hoscheit A M, Austin J K, Jones W L
J Am Optom Assoc. 1993 Aug;64(8):563-7.
Goodpasture's syndrome is a rare, rapidly fatal disease that consists of glomerulonephritis and pulmonary hemorrhage. Although not common, the ophthalmic manifestations of this disease include hemorrhagic and/or exudative retinopathy and infrequently, nonrhegmatogenous retinal detachment.
A 25-year-old white male was examined with a complaint of bilateral intermittent blurring of vision. His medical history revealed a diagnosis of Goodpasture's syndrome with subsequent renal failure and associated complications. Ophthalmoscopy and visual field testing demonstrated bilateral, inferior nonrhegmatogenous retinal detachments.
Optimum control of both blood pressure and metabolic processes were recommended to increase the chance of resolution of the nonrhegmatogenous retinal detachments.
Although infrequently seen in Goodpasture's syndrome, nonrhegmatogenous retinal detachment may have a good prognosis for recovery when diagnosed early and with treatment of the underlying disease and its metabolic derangements.
古德帕斯丘综合征是一种罕见的、迅速致命的疾病,由肾小球肾炎和肺出血组成。尽管这种疾病并不常见,但其眼部表现包括出血性和/或渗出性视网膜病变,罕见的情况下还包括非孔源性视网膜脱离。
一名25岁的白人男性因双侧间歇性视力模糊前来就诊。他的病史显示诊断为古德帕斯丘综合征,随后出现肾衰竭及相关并发症。眼底检查和视野测试显示双侧下方非孔源性视网膜脱离。
建议最佳控制血压和代谢过程,以增加非孔源性视网膜脱离消退的机会。
尽管在古德帕斯丘综合征中不常见,但非孔源性视网膜脱离如果早期诊断并治疗基础疾病及其代谢紊乱,可能有良好的恢复预后。