Pérez Martínez V M, Casanova Gómez M, Pérez Díaz L
An Esp Pediatr. 1977 Jan;10(1):81-7.
One case of anomalous origin of the right pulmonary artery from ascending aorta is reported. The anomalies in the origin of the main pulmonary branches are classified in Type A: Anomalous origin of a pulmonary artery from ascending aorta; Type B: Anomalous origin of a pulmonary artery from the aortic arch through a ductus arteriosus, and Type C: Absence of a pulmonary artery with pulmonary vasculariation through systemic arteries arising from descending aorta. The normal embryology of the 6th. aortic arch and the pulmonary branches and the differents theories postulated about the embryopathogenesis of these malformations are reviewed. The outstanding clinical, hemodynamic, angiocardiographic and surgical features are also discussed.
报告了1例右肺动脉起自升主动脉的病例。主肺动脉分支起源异常分为A 型：肺动脉起自升主动脉；B型：肺动脉通过动脉导管起自主动脉弓；C型：肺动脉缺如，肺血管由降主动脉发出的体循环动脉供应。回顾了第六对主动脉弓和肺动脉分支的正常胚胎发育过程以及关于这些畸形胚胎发病机制的不同假说。还讨论了其显著的临床、血流动力学、心血管造影和手术特征。
